Abstract
Fetal cardiac tumors are a rare entity. Here we report a neonate whose fetal ultrasonogram revealed a cardiac rhabdomyoma. Postnatally the baby had as hleaf macules in the skin, subependymal nodules and cortical tubers which eventually turned out be tuberous sclerosis. Fetal cardiac rhabdomyoma serves as a prenatal marker of tuberous sclerosis.
Key words: Rhabdomyoma, ash leaf macules, subependymal nodules, tuberous sclerosis.