Giant plexiform neurofibromatosis is a relatively rare manifestation of Type 1 neurofibromatosis. This condition leads to gross disfiguration along with functional disability. Due to the unpredictable natural history and high vascularity of these lesions, the optimal management is still not well defined. We are presenting a 20 year male of Plexifrom Neurofibromatosis of left upper limb. The aim of this rare case report is also to discuss the management difficulties encountered.
Plexiform Neurofibromatosis, Cfe-au-lait spot