Maffucci syndrome is a rare non hereditary disorder characterized by multiple enchondromas and hemangiomas. A 23 year old female presented to us with multiple nodular swellings over the left hand and a few bright red soft swellings over the left ear and oral cavity. They were found to be enchondromas and hemangiomas respectively. She also presented with a progressively increasing painless swelling over the left foot which on histology showed the features of composite hemangioendothelioma. It is a recently described unusual vascular tumour of low grade malignancy exhibiting a composite of hemangioendothelioma variants.
Maffucci syndrome, enchondroma, hemangioma, lymphangioma, hemangioendothelioma.