Myxoid neurothekeoma is a rare benign cutaneous neoplasm of nerve sheath origin. It usually arise in childhood and early adult life. It can occur in skin, soft tissue or intraspinal location. Most commonly involves head, neck and shoulder. This rare tumor is misdiagnosed as other more common benign neuronal tumors. It should be distinguished from certain malignant tumors like fibrohistiocytic tumors or plexiform cell tumors, neurotrophic melanomas and clear cell sarcoma. This case report describes a rare case of neurothekeoma presenting as scalp swelling in a 29 year old female. Clinically, it was diagnosed as sebaceous cyst. Hence it is important to be aware of this entity to avoid misdiagnosis.
Neurothekeoma, benign neoplasm, nerve sheath origin