Introduction: Clear cell sarcoma of soft tissue (CCSST) is a rare tumor accounting for less than 1% of all sarcomas. The most common location is extremities. We report an extremely rare case of CCSST of cervical cord region. Case Presentation: A 44 year old male patient presented with complaints of right neck swelling and pain cervical spine region radiating to right arm. Lymph node biopsy showed metastatic clear cell sarcoma of soft part (melanoma of soft part). Whole body PET CT scan reported metabolically active enlarged right posterior cervical lymph node and hypermetabolic focal lesion in right side of spinal canal The intraspinal tumor was unresectable so patient received External Beam Radiotherapy. Follow up MRI after six months reported stable disease. Conclusion: CCSST is a rare tumor and our patient had tumor location in cervical cord region which is an unusual location. In surgically inoperable case like this, radiotherapy may be considered as treatment option and it has resulted in symptom-free survival in this
patient till date.
Clear cell sarcoma, Intraspinal, cervical cord