Osteogenesis imperfecta is a rare inherited genetic disease characterized by increased bone fragility due to defective synthesis of the collagen molecule. Dentigerous cyst is the most common odontogenic developmental cyst associated with impacted teeth. Till date, in literature no association has been reported between the dentigerous cyst and osteogenesis imperfecta. Here in this case report, we present a rare case of osteogenesis imperfect a type 1A representing with multiple dentigerous cyst central type; the first case to be reported in the literature till date to the best of our knowledge.
Osteogenesis imperfect, dentigerous cyst, Blue sclera, mandibular prognathism.